Have a personal or library account? Click to login
Left Ventricular Non-compaction Cardiomyopathy and Polycystic Kidney Disease Revealed by Inappropriate Polycythemia: A Fortuitous Association? Case Report Cover

Left Ventricular Non-compaction Cardiomyopathy and Polycystic Kidney Disease Revealed by Inappropriate Polycythemia: A Fortuitous Association? Case Report

Open Access
|Jan 2023

Figures & Tables

Figure 1

Two-dimensional parasternal short axis echocardiography (end-systolic frame)—note the thickness of the lateral wall, which appears trabeculated
Two-dimensional parasternal short axis echocardiography (end-systolic frame)—note the thickness of the lateral wall, which appears trabeculated

Figure 2

Cardiac magnetic resonance imaging showing left ventricular non-compaction criteria
Cardiac magnetic resonance imaging showing left ventricular non-compaction criteria

Figure 3

Abdominal ultrasound showing bilateral polycystic kidney disease: (a) Right kidney; (b) Left kidney
Abdominal ultrasound showing bilateral polycystic kidney disease: (a) Right kidney; (b) Left kidney

Figure 4

Algorithm for the evaluation of patients with erythrocytosis
Algorithm for the evaluation of patients with erythrocytosis

Blood tests results

TestDay 1Day 3Day 7
Hemoglobin (g/dl)1818.717.8
Erythrocyte count (x106/mm3)6.176.476.24
Hematocrit (%)5658.755.8
Uric acid (mg/dl)9.68
Creatinine (mg/dl)1.481.431.42
eRFG (ml/min/1.73m2)525454
NT-proBNP (pg/ml) 2346
hs-cTnI (pg/ml)23.420.815.3
O2 pressure in arterial blood (mmHg)808792
Erythropoietin (IU/L) 40 (N:4.3-29)

Diagnostic criteria for left ventricular non-compaction cardiomyopathy

CriteriaDescription
Echocardiographic criteria

Chin et al. [11]1. Prominent trabeculations, deep recesses
2. LV free-wall thickness (ED) augmentation from base to apex
3. Gradual reduction in the X:Y ratio of myocardial thickness from the mitral valve level to the papillary muscle level (PSAX and apical views)
X – from the epicardial surface to the bottom of the trabeculations
Y – from the epicardial surface to the top of the trabeculations

Stöllberger and Finsterer [12]1. Two-layered myocardium with the non-compacted layer thicker than the compacted myocardial layer (ED)
2. >3 trabeculations bulging from the LV apical wall to the papillary muscle
3. Intertrabecular spaces perfused

Jenni et al. [13]1. Bilayered myocardium, multiple prominent trabeculations (ES)
2. Non-compacted to compacted ratio >2:1
3. LV cavity communication with the intertrabecular spaces demonstrated by color Doppler
4. No coexisting cardiac abnormalities

MRI criteria

Petersen et al. [14]Non-compacted to compacted ratio >2.3 (ED)

Jacquier et al. [15]LV trabecular mass >20% of the global mass
DOI: https://doi.org/10.2478/rjc-2022-0037 | Journal eISSN: 2734-6382 | Journal ISSN: 1220-658X
Language: English
Page range: 210 - 215
Published on: Jan 11, 2023
Published by: Romanian Society of Cardiology
In partnership with: Paradigm Publishing Services
Publication frequency: 4 issues per year

© 2023 Andreea Simona Hodorogea, Andrei Cristian Dan Gheorghe, Irina Pârvu, Ioan Tiberiu Nanea, And Gabriela Silvia Gheorghe, published by Romanian Society of Cardiology
This work is licensed under the Creative Commons Attribution 4.0 License.