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Incidental Detection of Adult Polysplenia Syndrome With Situs Inversus Totalis, Interrupted Inferior Vena Cava, and Bronchiectasis Cover

Incidental Detection of Adult Polysplenia Syndrome With Situs Inversus Totalis, Interrupted Inferior Vena Cava, and Bronchiectasis

Open Access
|Mar 2025

Figures & Tables

Figure 1

Computed tomography axial (A) and coronal (B) image depicting abdominal situs inversus with polysplenia axial image (C) demonstrating dextrocardia with right-sided cardiac chambers on left side and vice-versa. (D) Coronal image in minimum intensity projection showing left main bronchus to be shorter than right main bronchus. S: spleen; IVC: inferior vena cava; RA: right atrium; RV: right ventricle; LV: left ventricle

Figure 2

(A,B) Computed tomography coronal and sagittal view depicting drainage of hepatic veins into right atrium. Intrahepatic inferior vena cava was absent with azygous continuation and subsequent drainage into right atrium. RA: right atrium; HV: hepatic vein; SVC: superior vena cava; AzV: azygous vein

Figure 3

(A,B) Axial lung window image revealing cystic bronchiectasis in bilateral lungs. (C) Coronal noncontrast scan of paranasal sinuses revealed no evidence of sinusitis.

DOI: https://doi.org/10.14797/mdcvj.1537 | Journal eISSN: 1947-6108
Language: English
Page range: 6 - 9
Submitted on: Dec 21, 2024
Accepted on: Jan 22, 2025
Published on: Mar 6, 2025
Published by: Houston Methodist DeBakey Heart & Vascular Center
In partnership with: Paradigm Publishing Services

© 2025 Kanupriya Arora, Mansi Verma, Sushma Makhaik, published by Houston Methodist DeBakey Heart & Vascular Center
This work is licensed under the Creative Commons Attribution-NonCommercial 4.0 License.