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Incidental Detection of Adult Polysplenia Syndrome With Situs Inversus Totalis, Interrupted Inferior Vena Cava, and Bronchiectasis Cover

Incidental Detection of Adult Polysplenia Syndrome With Situs Inversus Totalis, Interrupted Inferior Vena Cava, and Bronchiectasis

Open Access
|Mar 2025

Abstract

Incidental detection of polysplenia associated with situs inversus totalis in an adult is rarely reported in literature.1,2 “Heterotaxy” refers to a wide spectrum of anomalies involving dysmorphism of thoracoabdominal organs across the right-left axis of the body. Polysplenia is observed in left isomerism along with bilateral bilobed bronchi and bilateral morphologic left atria. However, in this case, polysplenia was present without isomerism.

DOI: https://doi.org/10.14797/mdcvj.1537 | Journal eISSN: 1947-6108
Language: English
Page range: 6 - 9
Submitted on: Dec 21, 2024
Accepted on: Jan 22, 2025
Published on: Mar 6, 2025
Published by: Houston Methodist DeBakey Heart & Vascular Center
In partnership with: Paradigm Publishing Services

© 2025 Kanupriya Arora, Mansi Verma, Sushma Makhaik, published by Houston Methodist DeBakey Heart & Vascular Center
This work is licensed under the Creative Commons Attribution-NonCommercial 4.0 License.