Video 1
The patient from the discussed case presenting for office visit. With eyes closed, note pseudoathetosis with limited proprioception, as right-hand drifts toward face. Next note finger to nose testing with eyes open and then eyes closed, revealing visibly more pseudoataxia with eyes closed. During gait exam using cane, patient with unsteady station, dystonic right lower extremity and right hand, and impaired dorsiflexion of left foot while ambulating.
Table 1
Summary of Observational Studies Discussing Treatments for Sjogren’s Associated Sensory Ganglionopathy.
| STUDY | N | THERAPIES USED | OUTCOME |
|---|---|---|---|
| Molina et al., 1996 | Small series | IVIG | Short term symptomatic improvement |
| Pereira et al., 2016 | 13 | Corticosteroids, mycophenolate mofetil, hydroxychloroquine, IVIG, cyclophosphamide | Slight mRS worsening over 3 years |
| Khan et al., 2019 | 1 | Corticosteroids, cyclophosphamide, rituximab → MMF | Sustained functional recovery |