Figure 1

Figure 2

The parameters of cardiac catheterization
| Parameters of cardiac catheterization | Values |
|---|---|
| RV Max dP/dt [mmHg/sec] | 938 |
| RV Max dP/dt/P [l/sec] | 22 |
| HB [G/100 ml] | 9.56 |
| Cardiac Output [l/min] | 11:25 3.52 |
| Cardiac Index [l/min/m2] | 5.75 |
| Venous Site | PA |
| Heart Site | AO |
| Heart rate | 98.00 |
| Stroke Volume [ml/beat] | 35.97 |
| SVi [ml/beat/m2] | 58.73 |
| O2 consumption [ml/min] | 118.3 |
| Predicted Pulm Vasc Resist [dynes*sec/cm5] | 1.73 |
| Predicted Syst Vasc Resist [dynes*sec/cm5] | 27.42 |
| Pulm Vasc Resistance [dynes*sec/cm5] | 1.590,.91 |
| PVR IX [(dynes*sec/cm5)*m2)] | 974.44 |
| Total Pulm Resistance [dynes*sec/cm5] | 1.670.45 |
| TPR IX [(dynes*sec/cm5)*m2)] | 1.023.12 |
| Syst Vascular Resistance [dynes*sec/cm5] | 1.545.45 |
| SVR IX [(dynes*sec/cm5)*m2)] | 946.60 |
| TSR [dynes*sec/cm5] | 1.727.27 |
| TSR IX [(dynes*sec/cm5)*m2)] | 1.057.96 |
| PVR/SVR res ratio | 1.03 |
| TPR/TSR res ratio | 0.97 |
The dinamics of the efficiency criteria for Bosentan and Sildenafil treatment
| Parameters | Before Therapy | After 1 month | After 3 months | After 4 months |
|---|---|---|---|---|
| Heart rate beat/min | 93 | 99 | 72 | 75 |
| Blood pressure mm/Hg | 90/60 | 91/55 | 90/60 | 90/60 |
| Saturation O2 % hand/leg | 97/68 | 99/70 | 96/76 | 97/80 |
| 6MWT (six minutes walk test) steps | 420 | 427 | 485 | 500 |
| MeanPAP | 70 | 45 | 40–42 | 43 |
| RVSP | 70 | 45 | 42 | 43 |
| CI | 3.55 | 2.3 | 3.06 | 2.64 |