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Pulmonary Hypertension in Children - New Insights of Diagnosis and Management Cover

Pulmonary Hypertension in Children - New Insights of Diagnosis and Management

Open Access
|May 2022

Figures & Tables

Figure 1

Echocardiography. Tubular PAD 5–6 mm with laminar shunt right-left in systole and left-right in diastole. Aortic cross laminar flux. Significant right ventricle hypertrophy. TAPSE 1.6cm, without regurgitation in tricuspid valve. LAS, IVS without changes. Dilated inferior vena cava.
Echocardiography. Tubular PAD 5–6 mm with laminar shunt right-left in systole and left-right in diastole. Aortic cross laminar flux. Significant right ventricle hypertrophy. TAPSE 1.6cm, without regurgitation in tricuspid valve. LAS, IVS without changes. Dilated inferior vena cava.

Figure 2

CT angiography. Persistent arterial duct with large dimensions: length 7mm, diameter 9×7mm. Pulmonary artery dilatation, right atrium and right ventricle dilatation.
CT angiography. Persistent arterial duct with large dimensions: length 7mm, diameter 9×7mm. Pulmonary artery dilatation, right atrium and right ventricle dilatation.

The parameters of cardiac catheterization

Parameters of cardiac catheterizationValues
RV Max dP/dt [mmHg/sec]938
RV Max dP/dt/P [l/sec]22
HB [G/100 ml]9.56
Cardiac Output [l/min]11:25 3.52
Cardiac Index [l/min/m2]5.75
Venous SitePA
Heart SiteAO
Heart rate98.00
Stroke Volume [ml/beat]35.97
SVi [ml/beat/m2]58.73
O2 consumption [ml/min]118.3
Predicted Pulm Vasc Resist [dynes*sec/cm5]1.73
Predicted Syst Vasc Resist [dynes*sec/cm5]27.42
Pulm Vasc Resistance [dynes*sec/cm5]1.590,.91
PVR IX [(dynes*sec/cm5)*m2)]974.44
Total Pulm Resistance [dynes*sec/cm5]1.670.45
TPR IX [(dynes*sec/cm5)*m2)]1.023.12
Syst Vascular Resistance [dynes*sec/cm5]1.545.45
SVR IX [(dynes*sec/cm5)*m2)]946.60
TSR [dynes*sec/cm5]1.727.27
TSR IX [(dynes*sec/cm5)*m2)]1.057.96
PVR/SVR res ratio1.03
TPR/TSR res ratio0.97

The dinamics of the efficiency criteria for Bosentan and Sildenafil treatment

ParametersBefore TherapyAfter 1 monthAfter 3 monthsAfter 4 months
Heart rate beat/min93997275
Blood pressure mm/Hg90/6091/5590/6090/60
Saturation O2 % hand/leg97/6899/7096/7697/80
6MWT (six minutes walk test) steps420427485500
MeanPAP704540–4243
RVSP70454243
CI3.552.33.062.64
DOI: https://doi.org/10.47803/rjc.2020.31.4.893 | Journal eISSN: 2734-6382 | Journal ISSN: 1220-658X
Language: English
Page range: 893 - 896
Published on: May 5, 2022
Published by: Romanian Society of Cardiology
In partnership with: Paradigm Publishing Services
Publication frequency: 4 issues per year

© 2022 Ina Palii, Iulia Rodoman, Daniela Palega, Lucia Pirtu, Svetlana Sciuca, published by Romanian Society of Cardiology
This work is licensed under the Creative Commons Attribution 4.0 License.