A case report of prenatal diagnostics and surgical correction of pulmonary agenesis associated with total anomalous pulmonary venous connection and vascular ring

Delikatnyi, Maksym; Tammo, Raad; Morkovkina, Hanna; Teterin, Oleksandr; Yalynska, Tetyana; Sekelyk, Roman

doi:10.2478/rjc-2023-0016

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A case report of prenatal diagnostics and surgical correction of pulmonary agenesis associated with total anomalous pulmonary venous connection and vascular ring

Romanian Journal of Cardiology

Volume 33 (2023): Issue 3 (September 2023)

By: Maksym Delikatnyi, Raad Tammo, Hanna Morkovkina, Oleksandr Teterin, Tetyana Yalynska and Roman Sekelyk

Open Access

|Sep 2023

Abstract

Pulmonary agenesis is a rare malformation associated with congenital heart disease and may lead to a life-threatening condition and death without pre-planned surgical and medical support.

We report an unusual case of unilateral pulmonary agenesis in combination with total anomalous pulmonary venous connection, complete vascular ring, retroaortic, retroesophageal innominate vein, secondary atrial septal defect, which was prenatally identified by fetal ultrasound and magnetic resonance imaging, later confirmed by postnatal computed tomography.

References

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DOI: https://doi.org/10.2478/rjc-2023-0016 | Journal eISSN: 2734-6382 | Journal ISSN: 1220-658X

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Language: English

Page range: 107 - 111

Published on: Sep 21, 2023

Published by: Romanian Society of Cardiology

In partnership with: Paradigm Publishing Services

Publication frequency: 4 issues per year

Keywords:

Pulmonary agenesis,

total anomalous pulmonary venous connection,

vascular ring,

congenital cardiac malformation

Related subjects:

Surgery,

Pediatrics and juvenile medicine,

Paediatric cardiology

© 2023 Maksym Delikatnyi, Raad Tammo, Hanna Morkovkina, Oleksandr Teterin, Tetyana Yalynska, Roman Sekelyk, published by Romanian Society of Cardiology
This work is licensed under the Creative Commons Attribution 4.0 License.

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