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Ultrasonography, MRI and classic radiography of skin and MSK involvement in juvenile scleroderma Cover

Ultrasonography, MRI and classic radiography of skin and MSK involvement in juvenile scleroderma

Journal of Ultrasonography
Volume 20 (2020): Issue 83 (January 2020)
By: Marta Idzior,  Maria Sotniczuk,  Emil Michalski,  Piotr Gietka and  Iwona Sudoł-Szopińska  
Open Access
|Dec 2020

Figures & Tables

Fig. 1.

13 y.o. boy with jSS and developmental disorders of the left thigh, left forearm and hand. A. Clinical presentation; B. Gray-scale B-mode with 24 MHz probe shows ill-defined border between the cutis and subcutaneous tissue, their thickening and increased echogenicity, comparing to the contralateral healthy side (left part of the image). C. The affected side shows increased vascularity in SMI comparing to the avascular healthy side. D. Shear wave (SW) elastography on 18 MHz transducer with propagation map taken from the affected area in the subdermal tissue of the thigh and the corresponding contralateral healthy side show an average speed in this area 1.91 m/s with standard deviation (SD) 0.71 m/s. E. SW elastography on the contralateral healthy side was 1.18 m/s and SD 0.18 m/s. F. Strain elastography shows lower tissues elasticity of the affected side. G. Strain elastography on the healthy side, for comparison
13 y.o. boy with jSS and developmental disorders of the left thigh, left forearm and hand. A. Clinical presentation; B. Gray-scale B-mode with 24 MHz probe shows ill-defined border between the cutis and subcutaneous tissue, their thickening and increased echogenicity, comparing to the contralateral healthy side (left part of the image). C. The affected side shows increased vascularity in SMI comparing to the avascular healthy side. D. Shear wave (SW) elastography on 18 MHz transducer with propagation map taken from the affected area in the subdermal tissue of the thigh and the corresponding contralateral healthy side show an average speed in this area 1.91 m/s with standard deviation (SD) 0.71 m/s. E. SW elastography on the contralateral healthy side was 1.18 m/s and SD 0.18 m/s. F. Strain elastography shows lower tissues elasticity of the affected side. G. Strain elastography on the healthy side, for comparison

Fig. 2.

Calcifications in scleroderma. Plain film radiography (AP projection) reveals a collection of calcifications in the soft tissue at the distal phalanx ( A ), ultrasonography confirms calcification in this location ( B ) with twinkling artefact on PD ( C ) Courtesy of Pracoń et al. 14
Calcifications in scleroderma. Plain film radiography (AP projection) reveals a collection of calcifications in the soft tissue at the distal phalanx ( A ), ultrasonography confirms calcification in this location ( B ) with twinkling artefact on PD ( C ) Courtesy of Pracoń et al. 14

Fig. 3.

Calcinosis cutis in a 15-year-old male patient with scleroderma activity, or fibrosis of affected tissues. Such information would be highly appreciated by pediatricians.
Calcinosis cutis in a 15-year-old male patient with scleroderma activity, or fibrosis of affected tissues. Such information would be highly appreciated by pediatricians.

Fig. 4.

Whole body MRI in PD FS sequence, coronal views in a juvenile with scleromyositis: A. increased signal of paravertebral and gluteal muscles, B. increased signal of thigh muscles bilaterally (arrows)
Whole body MRI in PD FS sequence, coronal views in a juvenile with scleromyositis: A. increased signal of paravertebral and gluteal muscles, B. increased signal of thigh muscles bilaterally (arrows)

Classification of juvenile scleroderma(7)

Juvenile systemic sclerodermaJuvenile localized scleroderma
Juvenile systemic sclerosisMorphea
Diffuse cutaneous (dcSsc)Plaque morphea
Limited cutaneous (lcSsc)Keloidal morphea
Generalized morphea
Bullous morphea
Skin limited systemic sclerosisLinear scleroderma
(CREST syndrome)Linear morphea
En coup de sabre
Parry-Romberg syndrome - hemifacial atrophy
Overlap syndromeEosinophilic fasciitis
DOI: https://doi.org/10.15557/jou.2020.0054 | Journal eISSN: 2451-070X | Journal ISSN: 2084-8404
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Language: English
Page range: 311 - 317
Submitted on: Sep 30, 2020
Accepted on: Oct 26, 2020
Published on: Dec 18, 2020
Published by: MEDICAL COMMUNICATIONS Sp. z o.o.
In partnership with: Paradigm Publishing Services
Publication frequency: 4 issues per year
Keywords:
scleroderma,
juvenile,
ultrasonography,
musculoskeletal system,
skin
Related subjects:
Medicine,
Basic medical science,
Basic medical science, other

© 2020 Marta Idzior, Maria Sotniczuk, Emil Michalski, Piotr Gietka, Iwona Sudoł-Szopińska, published by MEDICAL COMMUNICATIONS Sp. z o.o.
This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

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