Overview of Restrictive Cardiomyopathies

Smitha Narayana Gowda; Hyeon-Ju Ali; Imad Hussain

doi:10.14797/mdcvj.1078

Overview of Restrictive Cardiomyopathies

Methodist DeBakey Cardiovascular Journal

Volume 18 (2022): Issue 2

By: Smitha Narayana Gowda , Hyeon-Ju Ali and Imad Hussain

Open Access

|Mar 2022

Abstract

Restrictive cardiomyopathy (RCM) includes a heterogeneous group of diseases that cause increased myocardial stiffness, leading to impaired ventricular relaxation and severe diastolic dysfunction. Given that it is the least common type of cardiomyopathy, it can be a diagnostic challenge due to its varied pathogenesis, clinical presentation, and diagnostic evaluation. In this review, we provide an overview of different etiologies of RCM and examine the diagnostic and treatment approaches for various types.

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Articles in this issue

DOI: https://doi.org/10.14797/mdcvj.1078 | Journal eISSN: 1947-6108

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Language: English

Page range: 4 - 16

Submitted on: Jan 3, 2022

Accepted on: Feb 10, 2022

Published on: Mar 14, 2022

Published by: Houston Methodist DeBakey Heart & Vascular Center

In partnership with: Paradigm Publishing Services

Keywords:

restrictive cardiomyopathy,

iron overload cardiomyopathy,

idiopathic RCM,

endomyocardial fibrosis,

radiation-induced cardiomyopathy,

Loeffler’s endocarditis,

Fabry’s disease

© 2022 Smitha Narayana Gowda, Hyeon-Ju Ali, Imad Hussain, published by Houston Methodist DeBakey Heart & Vascular Center
This work is licensed under the Creative Commons Attribution-NonCommercial 4.0 License.

Volume 18 (2022): Issue 2