Chronic Thromboembolic Pulmonary Hypertension: A Comprehensive Review and Multidisciplinary Approach to Surgical Treatment

Qasim Al Abri; Alexander J Lu; Mahesh K Ramchandani

doi:10.14797/IQTU6714

Chronic Thromboembolic Pulmonary Hypertension: A Comprehensive Review and Multidisciplinary Approach to Surgical Treatment

Methodist DeBakey Cardiovascular Journal

Volume 17 (2021): Issue 2

By: Qasim Al Abri, Alexander J Lu and Mahesh K Ramchandani

Open Access

|Jul 2021

Abstract

Chronic thromboembolic pulmonary hypertension (CTEPH) is an underdiagnosed and undertreated sequelae of acute pulmonary embolism. In this comprehensive review, we provide an introductory overview of CTEPH, highlight recent advances in its diagnostic imaging, and describe the surgical technique for pulmonary thromboendarterectomy (PTE), the only established curative treatment for CTEPH. We also discuss the emerging role of balloon pulmonary angioplasty, both independently and combined with PTE, for patients with inoperable, residual, or refractory pulmonary hypertension post PTE. Finally, we stress the importance of a specialized multidisciplinary team approach to CTEPH patient care and share our approach to optimizing care for these patients.

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Articles in this issue

DOI: https://doi.org/10.14797/IQTU6714 | Journal eISSN: 1947-6108

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Language: English

Submitted on: Apr 4, 2021

Accepted on: Apr 4, 2021

Published on: Jul 1, 2021

Published by: Houston Methodist DeBakey Heart & Vascular Center

In partnership with: Paradigm Publishing Services

Keywords:

chronic thromboembolic pulmonary hypertension,

pulmonary hypertension,

CTEPH,

pulmonary thromboendarterectomy,

balloon pulmonary angioplasty,

riociguat

© 2021 Qasim Al Abri, Alexander J Lu, Mahesh K Ramchandani, published by Houston Methodist DeBakey Heart & Vascular Center
This work is licensed under the Creative Commons Attribution-NonCommercial 4.0 License.

Volume 17 (2021): Issue 2