Table 1
Initial and most recent deep brain stimulation parameters.
| PARAMETER | INITIAL SETTINGS | MOST RECENT SETTINGS | ||
|---|---|---|---|---|
| LEFT | RIGHT | LEFT | RIGHT | |
| Contacts | 1+ 2 – | 10+ 11 – | 1+ 2 – | 10+ 11 – |
| Amplitude | 2.5 V | 2.5 V | 3.1 V | 2.9 V |
| Pulse width | 60 µs | 60 µs | 60 µs | 60 µs |
| Frequency | 130 Hz | 130 Hz | 130 Hz | 130 Hz |
Video 1
Taken prior to DBS implantation at age 31. The video shows a marked left torticollis and right laterocollis, with elevation of the right shoulder and evidence of a sensory trick. There is dystonic posturing of the right upper limb and evidence of task-specific dystonia on writing.
Video 2
In DBS ‘ON’ stage at 40 (8.5 years post DBS implantation). There is moderate left torticollis with restricted range of movement to right, and anterior sagittal shift.
Video 3
In DBS “OFF” state. Severe left torticollis with inability to turn the head past the midline to the right, with additional severe antecaput and truncal involvement. Significant tremulous dystonic posturing of both upper limbs is evident.