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The Effect of Low Dose OnabotulinumtoxinA on Cervical Dystonia in Hypermobile Ehlers-Danlos Syndrome Cover

The Effect of Low Dose OnabotulinumtoxinA on Cervical Dystonia in Hypermobile Ehlers-Danlos Syndrome

Open Access
|Oct 2021

Figures & Tables

Table 1

TWSTRS, SCM deep fascia thickness, and SCM deep fascia stiffness before and after OnabotulinumtoxinA injection.

PRE- INJECTIONPOST- INJECTIONSITES OF INJECTION
Average
TWSTRS52 ± 436 ± 8
    Torticollis Severity21 ± 54 ± 3
    Disability Scale17 ± 81 ± 4
    Pain Scale16 ± 212 ± 5
SCM Deep Fascia Thickness1.7 ± 0.5 mm1.2 ± 0.2 mm
Stiffness Deep Fascia to SCM Ratio1.10 ± 0.381.33 ± 0.48
Case 1R semispinalis capitus 10 units × 2
TWSTRS56.2536.25Fascial Plane Horizontal Intrarotation/Extrarotation:
    Torticollis Severity217L SCM near mastoid process 10 units
    Disability Scale1711L SCM near clavicle 10 units
    Pain Scale18.2518.25L Splenius Capitus near Transverse process of C2–4 10 units × 2
SCM Deep Fascia Thickness1.4 mm1.1 mmR Levator scapula 10 units × 2
Stiffness Deep Fascia to SCM Ratio0.860.97R Rhomboid minor at medial spine of scapula 10 units × 2
Case 2R semispinalis capitus 10 units × 2
TWSTRS4915Fascial Plane Diagonal Spiral Antemedial/retrolateral:
    Torticollis Severity263R/L alar nasalis 4 units × 2
    Disability Scale183L pectoralis minor at rib 2–4 4 units
    Pain Scale159L SCM near sternoclavicular joint 10 units
SCM Deep Fascia Thickness1.7 mm1.4 mmR Splenius capitus near C2–3 10 units × 2
Stiffness Deep Fascia to SCM Ratio1.331.46R upper trapezius border 10 units × 2
Case 3R semispinalis capitus 10 units × 2
TWSTRS5020.5Fascial Plane Horizontal Intrarotation/Extrarotation:
    Torticollis Severity172L Auricularis anterior 4 units
    Disability Scale179L SCM near mastoid process 10 units
    Pain Scale169.5L SCM near clavicle 10 units
SCM Deep Fascia Thickness1.9 mm1.2 mmL Splenius Capitus near Transverse process of C2–4 10 units × 2
Stiffness Deep Fascia to SCM Ratio1.121.56L Levator scapula 10 units
L Rhomboid minor at medial spine of scapula 10 units × 2
tohm-11-1-647-g1.jpg
Figure 1

The right sternocleidomastoid was selected for injection under standard cervical dystonia assessment. This corresponded with the right CF (blue dot) located at the insertion site of the sternocleidomastoid at the sternoclavicular joint- allowing for more specificity in injection site selection.

tohm-11-1-647-g2.jpg
Figure 2

Changes in deep fascia thickness before ONABOTULINUMTOXINA injection (A) and after ONABOTULINUMTOXINA injection (B) showing decrease in thickness.

DOI: https://doi.org/10.5334/tohm.647 | Journal eISSN: 2160-8288
Language: English
Submitted on: Jul 27, 2021
Accepted on: Oct 14, 2021
Published on: Oct 25, 2021
Published by: Ubiquity Press
In partnership with: Paradigm Publishing Services
Publication frequency: 1 issue per year

© 2021 Tina J. Wang, Antonio Stecco, Khashayar Dashtipour, published by Ubiquity Press
This work is licensed under the Creative Commons Attribution 4.0 License.