
Figure 1
Expansile mass in the upper portion of the left kidney (thick arrows in A, B, D), with invasion of the sinusal fat tissue (B, D). A delayed nephrogram is apparent secondary to outflow obstruction due to renal vein thrombosis (thin arrow in C). Large, confluent, retroperitoneal lymphadenopathies can be seen (arrowheads in B, C).

Figure 2
Gross specimen of the resected kidney.

Figure 3
A. H&E – Encapsulated tumor with tubulopapillary architecture. Tumor cells show eosinophilic cytoplasm and pleomorphic hyperchromatic nuclei with Fuhrmann nuclear grade 3. B. Immunohistochemistry markers with PAX8/panCK positivity.

Figure 4
Multiple skin papules/nodules on the upper arm, compatible with cutaneous leiomyoma.
