A rare case of pure cutaneous Rosai-Dorfman disease

Rosai-Dorfman disease (RDD) is a rare but usually benign non-Langerhans cell histiocytic disorder which commonly affects lymph nodes and frequently present with bilateral painless enlarged cervical lymph nodes with systemic symptoms. Although extra nodal tissue involvement is seen in considerable proportion, purely cutaneous involvement without affecting lymph nodes is very rare and forms a diverse clinical entity. Histopathology with immunohistochemical staining remains gold standard in diagnosing this rare entity. Different treatment modalities have been tried in case reports and treatment response is variable. Here we report a case of pure cutaneous RDD in a 21-yearold young female who was referred for staged excision.