Neuro Behcet’s disease

Behcet’s disease is a multisystem vasculitis of unknown aetiology, in which neurologic involvement has been reported in the range of 5% to 10%. We report a young patient, who presented with orogenital ulcers, brainstem dysfunction and positive pathergy reaction where the diagnosis of Neuro Behcet’s disease (parenchymal type) was made. His magnetic resonance imaging (MRI) showed bilateral lesions, mainly in brainstem, thalami and periventricular regions. He was successfully treated with immunosuppressive agents.