Dermatopathia pigmentosa reticularis (DPR): A rare case of late onset disease

Dermatopathia pigmentosa reticularis (DPR) is a rare inherited disorder presenting with the clinical triad of reticulate pigmentation, nail dystrophy and diffuse alopecia.

The usual presentation of DPR is at birth or very early childhood (<2 years). A few cases of late-onset disease have been reported. We report a rare case of post-pubertal onset disease, which had started at the age of seventeen years.