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Importance of molecular cell biology investigations in human medicine in the story of the Hutchinson-Gilford progeria syndrome Cover

Importance of molecular cell biology investigations in human medicine in the story of the Hutchinson-Gilford progeria syndrome

By: Ivan Raška  
Open Access
|Oct 2010

References

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  2. Capell BC, Olive M, Erdos MR, Cao K, Faddah DA, Tavarez UL, Conneely KN, Qu X, San H, Ganesh SK, Chen X, Avallone H, Kolodgie FD, Virmani R, Nabel EG, Collins FS. (2008). A farnesyltransferase inhibitor prevents both the onset and late progression of cardiovascular disease in a progeria mouse model. Proc Natl Acad Sci U S A 105(41): 15902-15907.
  3. Broers JL, Ramaekers FC, Bonne G, Yaou RB, Hutchison CJ. (2006). Nuclear Lamins: Laminopathies and Their Role in Premature Ageing. Physiol Rev 86(3): 967-1008.
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  6. Scaffidi P, Misteli T. (2005). Reversal of the cellular phenotype in the premature aging disease Hutchinson-Gilford Progeria Syndrome. Nat Med 11: 440-445.
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DOI: https://doi.org/10.2478/v10102-010-0018-y | Journal eISSN: 1337-9569 | Journal ISSN: 1337-6853
Language: English
Page range: 89 - 93
Published on: Oct 22, 2010
In partnership with: Paradigm Publishing Services
Publication frequency: 4 issues per year

© 2010 Ivan Raška, published by Slovak Academy of Sciences, Institute of Experimental Pharmacology & Toxicology, Centre of Experimental Medicine
This work is licensed under the Creative Commons License.

Volume 3 (2010): Issue 3 (September 2010)