Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour

Marek Wronski; Bogna Ziarkiewicz-Wroblewska; Maciej Slodkowski; Wlodzimierz Cebulski; Barbara Gornicka; Ireneusz Krasnodebski

doi:10.2478/v10019-010-0051-7

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Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour

Radiology and Oncology

Volume 45 (2011): Issue 1 (March 2011)

By: Marek Wronski, Bogna Ziarkiewicz-Wroblewska, Maciej Slodkowski, Wlodzimierz Cebulski, Barbara Gornicka and Ireneusz Krasnodebski

Open Access

|Nov 2010

Abstract

Introduction. Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easily confused with other primary gastrointestinal tumours, especially with that of the mesenchymal origin.

Case report. We report a case of a 44-year-old female who presented with an abdominal mass that radiologically and pathologically mimicked a gastrointestinal stromal tumour.

Conclusions. The diagnosis of mesenteric fibromatosis should always be considered in the case of mesenchymal tumours apparently originating from the bowel wall that diffusely infiltrate the mesentery.

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Articles in this issue

DOI: https://doi.org/10.2478/v10019-010-0051-7 | Journal eISSN: 1581-3207 | Journal ISSN: 1318-2099

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Language: English

Page range: 59 - 63

Published on: Nov 25, 2010

Published by: Association of Radiology and Oncology

In partnership with: Paradigm Publishing Services

Publication frequency: 4 issues per year

Keywords:

mesenteric fibromatosis,

desmoid tumour,

gastrointestinal stromal tumour,

GIST,

differential diagnosis

Related subjects:

Medicine,

Clinical medicine,

Internal medicine,

Haematology, oncology,

Radiology

© 2010 Marek Wronski, Bogna Ziarkiewicz-Wroblewska, Maciej Slodkowski, Wlodzimierz Cebulski, Barbara Gornicka, Ireneusz Krasnodebski, published by Association of Radiology and Oncology
This work is licensed under the Creative Commons License.

Volume 45 (2011): Issue 1 (March 2011)