Have a personal or library account? Click to login
Potocki-Lupski Syndrome Dup17p11.2 in a Girl with Hypotonia and Early Behavioural Disturbances Cover

Potocki-Lupski Syndrome Dup17p11.2 in a Girl with Hypotonia and Early Behavioural Disturbances

Open Access
|Oct 2021

References

  1. 1. Potocki L, Neira-Fresneda J, Yuan B.Potocki-Lupski Syndrome. In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, Amemiya A, editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2019. 2017 Aug 24.
  2. 2. Campbell IM, Shaw CA, Stankiewicz P, Lupski JR. Somatic mosaicism: implications for disease and transmission genetics. Trends Genet. 2015;31:382–92.10.1016/j.tig.2015.03.013449004225910407
  3. 3. Jefferies JL, Pignatelli RH, Martinez HR, Robbins-Furman PJ, Liu P, Gu W, Lupski JR, Potocki L. Cardiovascular findings in duplication 17p11.2 syndrome. Genet Med. 2012;14:90–4.10.1038/gim.0b013e3182329723366691922237436
  4. 4. Magoulas PL, Liu P, Gelowani V, Soler-Alfonso C, Kivuva EC, Lupski JR, Potocki L. Inherited dup(17)(p11.2p11.2): expanding the phenotype of the Potocki-Lupski syndrome. Am J Med Genet A. 2014;164A:500–4.10.1002/ajmg.a.3628724311450
  5. 5. Neira-Fresneda J, Potocki L. Neurodevelopmental disorders associated with abnormal gene dosage: Smith-Magenis and Potocki-Lupski Syndromes. J Pediatr Genet. 2015;4:159–67.10.1055/s-0035-1564443491872127617127
  6. 6. Walz K, Paylor R, Yan J, Bi W, Lupski JR. Rai1 duplication causes physical and behavioural pheno-types in a mouse model of dup(17)(p11.2p11.2). J Clin Invest. 2006;116:3035–41.10.1172/JCI28953159026917024248
  7. 7. Walz K, Spencer C, Kaasik K, Lee CC, Lupski JR, Paylor R. Behavioral characterization of mouse models for Smith-Magenis syndrome and dup(17) (p11.2p11.2). Hum Mol Genet. 2004;13:367–78.10.1093/hmg/ddh04414709593
  8. 8. Yuan B, Harel T, Gu S, Liu P, Burglen L, Chantot-Bastaraud S, Gelowani V, Beck CR, Carvalho CMB, Cheung SW, Coe A, Malan V, Munnich A, Magoulas PL, Potocki L, Lupski JR. Nonrecurrent 17p11.2p12 rearrangement events that result in two concomitant genomic disorders: the PMP22-RAI1 contiguous gene duplication syndrome. Am J Hum Genet. 2015;97:691–707.10.1016/j.ajhg.2015.10.003466713126544804
  9. 9. Potocki L, Bi W, Treadwell-Deering D, Carvalho CMB, Eifert A, Friedman EM, Glaze D, Krull K, Lee JA, Lewis RA, Mendoza-Londono R, Robbins-Furman P, Shaw C, Shi X, Weissenberger G, Withers M, Yatsenko SA, Zackai EH, Stankiewicz P, Lupski JR. Characterization of Potocki-Lupski syndrome (dup(17)(p11.2p11.2)) and delineation of a dosage-sensitive critical interval that can convey an autism Phenotype. Am J Hum Genet. 2007;80:633–49.10.1086/512864185271217357070
  10. 10. Potocki L, Chen K-S, Park S-S, Osterholm DE, Withers MA, Kimonis V, Summers AM, Meschino WS, Anyane-Yeboa K, Kashork CD, Shaffer LG, Lupski JR. Molecular mechanism for duplication 17p11.2 - the homologous recombination reciprocal of the Smith-Magenis microdeletion. Nat Genet. 2000;24:84–7.10.1038/7174310615134
  11. 11. Soler-Alfonso C, Motil KJ, Turk CL, Robbins-Furman P, Friedman EM, Zhang F, Lupski JR, Fraley JK, Potocki L. Potocki-Lupski syndrome: A microduplication syndrome associated with oropharyngeal dysphagia and failure to thrive. J Pediatr. 2011;158:655–9.e2.10.1016/j.jpeds.2010.09.062305937021168152
  12. 12. Treadwell-Deering DE, Powell MP, Potocki L. Cognitive and behavioural characterization of the Potocki-Lupski syndrome (duplication 17p11.2). J Dev Behav Pediatr. 2010;31:137–43.10.1097/DBP.0b013e3181cda67e20110824
  13. 13. Yusupov R, Roberts AE, Lacro RV, Sandstrom M, Ligon AH. Potocki-Lupski syndrome: An inherited dup(17)(p11.2p11.2) with hypoplastic left heart. Am J Med Genet A. 2011;155A:367–71.10.1002/ajmg.a.3384521271656
DOI: https://doi.org/10.2478/prilozi-2021-0026 | Journal eISSN: 1857-8985 | Journal ISSN: 1857-9345
Language: English
Page range: 91 - 94
Published on: Oct 26, 2021
Published by: Macedonian Academy of Sciences and Arts
In partnership with: Paradigm Publishing Services
Publication frequency: 2 issues per year

© 2021 Orhideja Stomnaroska, Lidija Neskovska, published by Macedonian Academy of Sciences and Arts
This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 License.