Critical Neonatal Congenital Heart Disease – a Rare Complication after Successful Surgical Correction

Carmen Corina Şuteu; Iolanda Muntean; Cristina Blesneac; Marian Pop; Rodica Togănel

doi:10.2478/jce-2020-0019

Abstract

Pulmonary arterial hypertension (PAH) is a rare but severe complication that should be investigated in patients diagnosed with transposition of the great arteries who have undergone neonatal arterial switch operation. Early diagnosis and aggressive combination therapy for PAH could help to improve survival in these patients. We report a favorable clinical response 6 months after the initiation of vasodilator therapy in a pediatric case with transposition of the great arteries, successfully repaired in the neonatal period, who developed pulmonary arterial hypertension at the age of 5 years.

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Critical Neonatal Congenital Heart Disease – a Rare Complication after Successful Surgical Correction

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