Have a personal or library account? Click to login
Otopalatodigital syndrome type I: novel characteristics and prenatal manifestations in two siblings Cover

Otopalatodigital syndrome type I: novel characteristics and prenatal manifestations in two siblings

Open Access
|Dec 2019

References

  1. Robertson SP. Otopalatodigital syndrome spectrum disorders: Otopalatodigital syndrome types 1 and 2, fronto-metaphyseal dysplasia and Melnick-Needles syndrome. Eur J Hum Genet. 2007; 15(1): 3-9.
  2. Robertson S. In: Adam MP, Ardinger HH, Pagon RA, Wallace Se, Bean LJH, Stephens K, et al. (editors). X-Linked Otopalatodigital Spectrum Disorders (1993-2019). GeneReviews® [Internet]. Seattle, WA, USA: University of Washington, Seattle; 2005 [updated 2019].
  3. Clark AR, Sawyer GM, Robertson SP, Sutherland-Smith AJ. Skeletal dysplasias due to filamin A mutations result from a gain-of-function mechanism distinct from allelic neurological disorders. Hum Mol Genet. 2009; 18(24): 4791-4800.
  4. Robertson S, Twigg S, Sutherland-Smith A, Biancalana V, Gorlin R, Horn D, et al. The OPD Spectrum Disorders Clinical Collaborative Group. Localized mutations in the gene encoding the cytoskeletal protein filamin A cause diverse malformations in humans. Nat Genet. 2003; 33(4): 487-491.
  5. Le Marec B, Odent S, Bracq E, Bulard MB, Bourdinière J, Babut JM. Oto-palato-digital type I syndrome in five generations. Relationship to the type II form. Ann Genet. 1988; 31(3): 155-161.
  6. Dudding BA, Gorlin RJ, Langer LO. The oto-palato-digital syndrome. A new symptom-complex consisting of deafness, dwarfism, cleft palate, characteristic facies, and a generalized bone dysplasia. Am J Dis Child. 1967; 113(2): 214-221.
  7. Robertson SP, Thompson S, Morgan T, Holder-Espinasse M, Martinot-Duquenoy V, Wilkie AO, et al. Postzygotic mutation and germline mosaicism in the oto-palatodigital syndrome spectrum disorders. Eur J Hum Genet. 2006; 14(5): 549-554.
  8. Murphy-Ryan M, Babovic-Vuksanovic D, Lindor N. Bifid tongue, corneal clouding, and Dandy-Walker malformation in a male infant with otopalatodigital syndrome type 2. Am J Med Genet A. 2011; 155A(4): 855-859.
  9. Naudion S, Moutton S, Coupry I, Sole G, Deforges J, Guerineau E, et al. Fetal phenotypes in otopalatodigital spectrum disorders. Clin Genet. 2016; 89(3): 371-377.
  10. Mariño-Enríquez A, Lapunzina P, Robertson SP, Rodríguez JI. Otopalatodigital syndrome type 2 in two siblings with a novel filamin A 629G>T mutation: Clinical, pathological, and molecular findings. Am J Med Genet A. 2007; 143A(10):1120-1125.
  11. Femitha P, Joy R, Gane BD, Adhisivan B, Bhat BV. Frank-ter Haar Syndrome in a newborn. Indian J Pediatr. 2012; 79(8): 1091-1093.
Language: English
Page range: 83 - 88
Published on: Dec 21, 2019
In partnership with: Paradigm Publishing Services
Publication frequency: 2 issues per year

© 2019 I Joksic, G Cuturilo, A Jurisic, S Djuricic, B Peterlin, M Mijovic, Orlic N Karadzov, A Egic, Z Milovanovic, published by Macedonian Academy of Sciences and Arts
This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.