Abstract
Sphenoid sinus affections in children are very rare occurrences due to the late development of the sinus and treatment may present quite a challenge even to the most skillful surgeon because of the small nasal fossae. Due to the often vague and uncharacteristic symptomatology sphenoid sinus disease is misdiagnosed and the treatment is delayed, sometimes with serious complications that are life threatening if not properly managed. We present the case of a six year old patient with a mucocele affecting an unusually large sphenoid sinus with concomitant Graves-like ophthalmopathy that has been treated through functional endoscopic sinus surgery but also needed prolonged cortisonic treatment.