Hepatopulmonary Syndrome: A Brief Review

Zulkifli Amin; Hilman Zulkifli Amin; Nadim Marchian Tedyanto

doi:10.1515/rjim-2016-0015

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Hepatopulmonary Syndrome: A Brief Review

Romanian Journal of Internal Medicine

Volume 54 (2016): Issue 2 (June 2016)

By: Zulkifli Amin, Hilman Zulkifli Amin and Nadim Marchian Tedyanto

Open Access

|May 2016

Abstract

Hepatopulmonary syndrome (HPS) is a pulmonary complication of liver disease characterized by arterial hypoxemia. Mechanisms related to this event are diffusion-perfusion flaw, ventilation-perfusion (V/Q) mismatch, and direct arteriovenous shunts. Diagnosis of HPS is based on the presence of liver disease or portal hypertension, increased alveolar-arterial (A-a) PO₂, and intrapulmonary vascular dilatations (IPVD). Lung transplantation (LT) remains the most effective therapy for HPS. In spite of its poor prognosis, we could improve the quality of life and survival rate of patients.

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Articles in this issue

DOI: https://doi.org/10.1515/rjim-2016-0015 | Journal eISSN: 2501-062X | Journal ISSN: 1220-4749

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Language: English

Page range: 93 - 97

Submitted on: Oct 9, 2015

Published on: May 20, 2016

Published by: N.G. Lupu Internal Medicine Foundation

In partnership with: Paradigm Publishing Services

Publication frequency: 4 issues per year

Keywords:

Hepatopulmonary syndrome,

Related subjects:

Internal medicine, other,

Cardiology,

Gastroenterology,

Rheumatology

© 2016 Zulkifli Amin, Hilman Zulkifli Amin, Nadim Marchian Tedyanto, published by N.G. Lupu Internal Medicine Foundation
This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Volume 54 (2016): Issue 2 (June 2016)